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G71.3

Billable

Mitochondrial myopathy, not elsewhere classified

G71.3 is the ICD-10-CM code for Mitochondrial myopathy, not elsewhere classified. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
G00-G99
Parent
G71
Edition
FY2026

G00-G99 Diseases of the nervous system

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What this means — in plain language

MedlinePlus · NIH

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder , something goes wrong with this process.…

Read more about Mitochondrial Diseases at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

Excludes1 — not coded here

  • •Kearns-Sayre syndrome (H49.81)
  • •Leber's disease (H47.21)
  • •Leigh's encephalopathy (G31.82)
  • •mitochondrial metabolism disorders (E88.4.-)
  • •Reye's syndrome (G93.7)

Medications indicated for this condition

FDA labeling

Drugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.

Conditions mapped to this code

MedlinePlus · NIH
Muscular DystrophyMitochondrial Diseases

Plain-language health-topic references grounded in MedlinePlus (NIH/NLM).

Benefits & assistance programs

Federal & state

Assistance programs whose eligibility maps to this condition's category. Informational only — eligibility is determined by the administering agency.

Frequently asked questions

What is ICD-10 code G71.3?
G71.3 is the ICD-10-CM code for "Mitochondrial myopathy, not elsewhere classified". It falls under G00-G99 Diseases of the nervous system.
Is G71.3 a billable code?
Yes — G71.3 is a billable, specific ICD-10-CM code valid for reimbursement.
What is excluded from G71.3?
Excludes1 (not coded here): Kearns-Sayre syndrome (H49.81); Leber's disease (H47.21); Leigh's encephalopathy (G31.82); mitochondrial metabolism disorders (E88.4.-).

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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