Caring for someone with this diagnosis? Eleplan keeps diagnoses, medications, documents and every specialist in one plan.
Start free with EleplanUrinary tract arteriovenous malformation
ORPHA:693872Malformation syndrome
Also called Arteriovenous malformation of the urinary tract
What it is
A rare visceral arteriovenous malformation characterized by abnormal communication between veins and arteries of the ureter, urethra, or urinary bladder. Major clinical signs include hematuria and suprapubic pain. Additional clinical features may include acute urinary retention and increased urinary frequency.
Key facts
- Age of onset
- Antenatal, Infancy, Neonatal
- Inheritance
- Not applicable
- Classified as
- Malformation syndrome
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
Powered by Eleplan
A rare diagnosis is just the start. Eleplan keeps the whole care plan in one place.
Diagnoses, medications, documents, appointments, and the whole care team — organized and always in sync, so you are not retelling the same story to every new specialist. With Ellie, your AI care assistant, on top of it. Free to start.